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Community Connections Home > Disabilities > About > Hydrocephalus


Specific DisabilitiesOverview

Hydrocephalus is an abnormal accumulation of fluid within cavities called "ventricles" inside the brain.  It's name comes from the Greek: "hydro" means water, "cephalus" means head.   Hydrocephalus occurs when there is an imbalance between the amount of cerebrospinal fluid (CSF) that is produced and the rate at which it is absorbed.

Types

Hydrocephalus may be congenital or acquired. Congenital hydrocephalus is present at birth, while acquired hydrocephalus develops at the time of birth or at some point afterward.

Hydrocephalus may also be "communicating" or "obstructive".  Communicating hydrocephalus occurs when the flow of CSF is blocked after it exits from the ventricles. This form is called "communicating" because the CSF can still flow between the ventricles, which remain open.  Non-communicating hydrocephalus - also called "obstructive"
hydrocephalus - occurs when the flow of CSF is blocked along one or more of the narrow pathways connecting the ventricles.

Causes

The causes of hydrocephalus are not all well understood.  Hydrocephalus that is congenital is thought to be caused by a both environmental and genetic factors, and is believed to occur in about 2 out of 1,000 births.   Among the possible causes of congenital hydrocephalus:

Congenital Hydrocephalus is believed to occur in about 2 out of 1,000 births.

Acquired hydrocephalus can affect individuals of all ages and may result from head injury/trauma or disease.  The incidences of adult-onset hydrocephalus and acquired hydrocephalus are not known.

Diagnosis/Characteristics

In early infancy hydrocephalus is usually detected by the family or pediatrician as a rapidly enlarging head. This may or may not be associated with symptoms such as vomiting, failure to thrive, irritability, delay or loss of developmental milestones.

Symptoms of hydrocephalus vary with age, disease progression, and individual differences in tolerance to CSF.  Older children and adults may experience different symptoms because their skulls cannot expand to accommodate the buildup of CSF. In older children or adults, symptoms may include headache followed by vomiting, nausea, papilledema (swelling of the optic disk which is part of the optic nerve), blurred vision, (double vision), problems with balance, poor coordination, gait disturbance, urinary incontinence, slowing or loss of development, lethargy, drowsiness, irritability, or other changes in personality or cognition including memory loss.

Some other terms or diagnoses for Hydrocephalus include:

Treatment

While hydrocephalus is very treatable, the underlying cause may not be or may have caused irreversible damage to the brain. It is important for the doctors taking care of a child with hydrocephalus to determine if the problem is ongoing or if it has resolved but left enlarged but stable ventricles. This can sometimes be difficult to tell and often the decision will be based on many factors including symptoms, eye exams, changes in level of activity or school performance. In addition to this often the child will have repeated (serial) radiographic exams to look for changes in the ventricles.

The most effective treatment is surgical insertion of a shunt - a flexible tube placed into the ventricular system that diverts the flow of CSF into another region of the body where it can be absorbed, such as the peritoneal (abdominal) cavity or the right atrium of the heart.

Endoscopic third ventriculostomy (ETV) is growing in popularity as an alternative treatment method for hydrocephalus - the surgery involves making a hole in the floor of the third ventricle to allow free flow of spinal fluid into the basal cisterns for absorption.

Prognosis

Prior to the advent of computerized axial tomography (CAT scans), the prognosis for children with hydrocephalus was generally poor. It was believed that an abbreviated life span would be plagued by numerous shunt revisions and associated complications. There was little optimism concerning physical and intellectual well-being over the course of a lifetime; both parents and physicians were exasperated by the many problems associated with the equipment available to manage the condition.  The CAT scan has changed this situation enormously. Most parents can now look forward to the likelihood of normal longevity with little or no intellectual or physical impairment.  While the prognosis for successful management of hydrocephalus is excellent, it is however the underlying cause that will ultimately determine a child's
outcome.

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Listings in Community Connections and events on the Community Calendar come from a variety of host organizations and individuals.  For information about events, please contact the event sponsor.  The distribution of information  via Community Connections does not imply sponsorship or endorsement of any specific organization or event by The Arc of King County, the King County Developmental Disabilities Division, or affiliated entities.

Community Connections is made possible with support from the King County Developmental Disabilities Division and is hosted by The Arc of King County.

This page last updated:  Sunday, November 25, 2007

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